J Med Cases

Journal of Medical Cases, ISSN 1923-4155 print, 1923-4163 online, Open Access

Article copyright, the authors; Journal compilation copyright, J Med Cases and Elmer Press Inc

Journal website https://www.journalmc.org

Case Report

Volume 13, Number 5, May 2022, pages 235-239

Idiopathic Pleuroparenchymal Fibroelastosis

Figures

Figure 1. Chest X-ray posterior-anterior (a) and lateral (b) views showing cardiomegaly, pulmonary vascular congestions, and small bilateral pleural effusions (red arrows).

Figure 2. Coronal (a) and axial (b) computed tomography (CT) scan of the chest demonstrating bilateral apical pleural thickening (green arrows).

Figure 3. Computed tomography (CT) scan of the chest showing upper lobe predominant interstitial lung disease with thickened pleura (blue arrows), as well as traction bronchiectasis, basilar reticulations, and honeycombing (red arrows). Right lung opacities (green arrows) are observed in the location of the prior radiation treatment.

Table

**Table 1.** Initial Laboratory Results
Serum test	Results	Reference range
White blood cells (× 10³/µL)	9.9	4.5 - 11.0
Hemoglobin (g/dL)	13.3	12.0 - 16.0
Mean corpuscular volume (fL)	95.5	80.0 - 100.0
Platelet count (× 10³/µL)	124	140 - 450
Glucose (mg/dL)	137	136 - 145
Blood urea nitrogen (mg/dL)	13	5 - 25
Creatinine (mg/dL)	0.73	0.44 - 1.0
Sodium (mmol/L)	137	135 - 146
Potassium (mmol/L)	3.3	3.5 - 5.2
Chloride (mmol/L)	96	96 - 110
Bicarbonate (mmol/L)	32	24 - 31
Alkaline phosphatase (U/L)	169	38 - 126
Total protein (g/L)	5.7	6.0 - 8.0
Albumin (g/dL)	2.6	3.5 - 5
Bilirubin, total (mg/dL)	1.6	0.2 - 1.3
Aspartate aminotransferase (U/L)	91	10 - 42
Alanine aminotransferase (U/L)	97	10 - 60
Procalcitonin (ng/mL)	0.33	< 0.50
Streptococcus pneumoniae, urine antigen	Negative	Negative
Legionella, urine antigen	Negative	Negative
Respiratory pathogen panel	Negative	Negative
QuantiFERON-TB	Negative	Negative
1,3-β-d-glucan (pg/mL)	< 31	< 60