Pulmonary Thromboembolism Following Splenectomy in Hereditary Spherocytosis

Abstract

Hereditary spherocytosis is an inherited disorder characterized by presence of spherocytes. It usually manifests clinically as triad of anaemia, splenomegaly and jaundice. The recommended treatment in a symptomatic patient is splenectomy. Occurrence of pulmonary thromboembolism in hereditary spherocytosis following splenectomy is unusual. We report the case of a 30-year-old male who underwent splenectomy for hereditary spherocytosis and subsequently developed pulmonary thromboembolism and right ventricular mural thrombosis six years later. His showed no other procoagulant disorders. The development of pulmonary thromboembolism and right ventricular mural thrombosis in a patient of hereditary spherocytosis after splenectomy is an interesting association.




J Med Cases. 2010;1(1):14-15
doi: https://doi.org/10.4021/jmc2010.06.102e