Unusual Presentation of a Dysembryoplastic Neuroepithelial Tumor Mimicking a Pontomesencephalic Cavernous Hemangioma

Abstract

Dysembryoplastic neuroepithelial tumor is a rare benign neoplasm that usually occurs in children and young adults and is characterized by intractable seizures that are refractory to medication. Since its description and inclusion in the World Health Organization classification of brain tumors, an increasing number of cases have been reported. The tumor is preferentially, but not exclusively, located in the supratentorial cortex. Rare cases of other locations have been reported. We describe the clinical, imaging and pathologic features of a case of dysembryoplastic neuroepithelial tumor arising in the pons of a 26-year-old woman, an unusual extracortical location, mimicking a cavernous hemangioma.




J Med Cases. 2012;3(6):375-378
doi: https://doi.org/10.4021/jmc718w